Cystic Fibrosis Guidelines

When studying about cystic fibrosis, you need to be properly guided. There are various pieces of information   you need to know about the disease.  The cystic fibrosis guidelines given below will be very helpful when you take time to go through them.


Definition Guideline

The first guide you need about cystic fibrosis is to know what it is.   Actually, it’s a hereditary or genetic disorder transferred in a family lineage.  It usually causes thick and stick mucus which starts to build around the vital organs affected. In most cases, the disease affects the lungs, pancreas, liver, digestive tract and other parts of the internal body system.



Cystic fibrosis is mainly caused by a defective gene.  This usually leads the body into the production of thick and stick mucus around the cells of the affected organ. The mucus continues to build up and also leads to several complications.  A child can easily pick up the disease from his or her parents.   Both parents must be carriers of the trait before the child can contact that.  The building of the mucus around the vital organs such as lungs and pancreas can lead to several infections.



Guideline on the Symptoms

The symptoms of cystic fibrosis abound.  They showcase in the lives of the baby or adult involved.

The basic symptoms in babies include:

  • Retarded or delayed growth
  • Weight loss
  • Improper bowel movement
  • Salty sweat
  • Breathing difficulty
  • Heart attack
  • Bloating of the stomach
  • Nausea
  • Loss of appetite
  • Greasy or pale stool.


The child may also have symptoms relating to the sinuses and lungs. Among them include:

  • Prolonged coughing
  • Fatigue
  • Congestions in the nose
  • Pneumonia
  • Fever
  • Shortness of breath
  • Sinus pain


Cystic Fibrosis symptoms in adult also abound. Among them include

  • Breathing difficulty
  • Infertility in men
  • Inflammation of the lungs
  • Inflammation of the pancreas
  • Respiratory problems and a lot more.


Treatment Guideline

Actually, cystic fibrosis has no cure.  Several attempts have been made by scientists and medical professionals in curing the disease, yet no real success has been achieved.  However, the disease can be adequately controlled.

The first step towards the control of the disease is the diagnosis.   Among the tests used in diagnosing it include:

  • Sweat test

This is very common. It’s used to measure the level of the sodium chloride or salt in the sweat of the individual affected.


  • Blood test

This is used to detect the presence of cystic fibrosis in the body system of the individual.


  • Genetic test

This is carried out to detect the presence of the disease in the gene make-up of the individual.


  • Immunoreactive Trypsinogen (IRT)

This is used as a screening test for   newborn babies who are suspected to have cystic fibrosis.


  • Some other tests used in diagnosing the disease include sputum culture test, fecal fat test, Chest x-ray, Lung function test, and Pancreatic function test.


Another guideline you need under the treatment session is how to cope with the disease.  In most cases, medical professionals can treat the various organs affected by the disease.  Certain antibiotics and other medications are usually recommended.  There are also inhaled medications used in correcting the airways.  Some vaccinations may also be given. It’s always important to go for regular checkups in order to checkmate the damages that may be done by the disease.

Finally, there’s a need to cope with the disease by joining   interest groups.  People living with cystic fibrosis are also advised to desist from smoking and exposure to dust, fumes, fire, smoke and other household chemicals.  Some physical exercises are also required in coping with the ailment.

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